Generalized Lymphangiomatosis Presenting as Cardiomegaly
نویسندگان
چکیده
منابع مشابه
Generalized Lymphangiomatosis: A Case Report
Generalized lymphangiomatosis is the term used for diffuse involvement of soft tissue, viscera (especially lungs and spleen) or bone by a lymphangiomatous proliferation. The presentation, as in our case, is often with a chylothorax. It is categorized as a subtype of lymphangiectasia, which is owing to dilatation, and proliferation of lymphatics (1). Lymphangiomatosis generally presents in the f...
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Lymphangiomatosis is a rare disorder of the lymphatic system that is known to cause chylothorax. Chyloptysis may occur but chylous bronchial cast formation is rare. A case is reported of lymphangiomatosis in a 34 year old woman whose initial manifestation was cough productive of bronchial casts. Two years later the patient developed a chylothorax. Ligation of the thoracic duct through a low tho...
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A female infant with generalized GM1-gangliosidosis differing in several aspects from previously reported cases is described. Clinically she is the first case to have cardiomegaly, unilateral congenitial dislocation of the hip and normal facial appearance. She had a higher residual leucocyte 13-galactosidase activity towards two synthetic substrates, namely p-nitrophenyl-f3-D-galactoside (PNP-1...
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are well documented but uncommon.[2,4] The lesions of SCAP measure between 1 and 3 cm in diameter[3] and all published cases of nodular SCAP have to date measured <4 cm in diameter.[4] A vast majority of SCAPs are solitary lesions, and linear arrangement of these lesions is particularly rare.[5] In 2001, Patterson et al., described that there had been only eight previous cases of linear SCAP. F...
متن کاملBilateral orbital lymphangiomas in two patients with generalized lymphangiomatosis.
SUMMARY Generalized lymphangiomatosis is a rare congenital malformation of the lymphatics, characterized by cystic lesions in parenchymal organs and lytic bone lesions. In this report, we describe the radiographic and clinical features of 2 unusual cases of generalized lymphangiomatosis with bilateral orbital involvement.
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ژورنال
عنوان ژورنال: Journal of the Formosan Medical Association
سال: 2007
ISSN: 0929-6646
DOI: 10.1016/s0929-6646(09)60359-4